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Pulmonary Hypertension Definition
- Pulmonary hypertension is defined as mean pulmonary artery pressure > 20 mmHg.
- Pulmonary arterial hypertension (PAH) is a subgroup with specific hemodynamic criteria including pulmonary vascular resistance >= 3 Wood units.
PAH Pathophysiology
- Vascular remodeling, including plexiform lesions and elastic lamina fragmentation, increases pulmonary vascular resistance.
- This leads to higher pulmonary artery pressure and right heart strain, causing right heart failure.
PAH Prevalence
- PAH is uncommon, with varying prevalence depending on the registry.
- US registries show an incidence of ~2 cases per million per year and prevalence ~10.6 per million adults.