Tetralogy of Fallot with Pulmonary Stenosis with Dr. Laura Ortmann
Nov 14, 2022
auto_awesome
Dr. Laura Ortmann, an associate professor and the Medical Director of the Cardiovascular Intensive Care Unit at Children's Hospital and Medical Center, discusses topics related to Tetralogy of Fallot with Pulmonary Stenosis. The podcast covers surgical procedures, bedside approaches for managing arrhythmias, postoperative care considerations, feeding intolerance, long-term complications, and the historical significance of repairing Tetralogy of Fallot.
The severity of pulmonary stenosis in Tetralogy of Fallot determines the degree of cyanosis, with different surgical options ranging from complete repair to palliative procedures depending on the level of cyanosis and comorbidities.
Post-operative care for Tetralogy of Fallot patients should include monitoring for complications such as arrhythmias and right ventricular dysfunction, optimizing fluid balance and RV preload, considering early extubation to improve RV function, and planning for long-term complications and potential interventions.
Deep dives
Understanding Tetralogy of Fallot
Tetralogy of Fallot is a common and complex cardiac defect characterized by four specific abnormalities related to the right ventricle, pulmonary artery, and aorta. These include pulmonary stenosis, ventricular septal defect (VSD), overriding aorta, and right ventricular hypertrophy. These defects arise from a common embryologic error involving the faulty development of the conal septum, leading to malalignment and resulting in these specific abnormalities. The severity of the pulmonary stenosis determines the degree of cyanosis in affected infants. The surgical options for Tetralogy of Fallot vary based on the degree of cyanosis and comorbidities. Neonates with severe cyanosis may require palliative procedures, such as an arterial-to-pulmonary shunt, before complete repair. In contrast, pink Tetralogy of Fallot infants who are less cyanotic typically undergo complete repair as neonates. The goals of Tetralogy of Fallot repair include creating unobstructed pulmonary blood flow and closing the VSD. In cases where the pulmonary valve annulus is narrow, a transannular patch may be necessary, resulting in pulmonary insufficiency that may require re-operation in the future. Monitoring for complications postoperatively is important, such as right ventricular diastolic dysfunction and arrhythmias like junctional ectopic tachycardia. Extubation can be considered in postoperative Tetralogy patients to optimize cardiac output and reduce RV afterload. Discharge planning should include close monitoring of fluid balance, feeding tolerance, and awareness of potential late-onset RV dysfunction.
Common Complications and Challenges
Complications and challenges associated with Tetralogy of Fallot include RV diastolic dysfunction, feeding intolerance, and potential late-onset RV dysfunction. RV diastolic dysfunction can lead to low cardiac output and hypotension, requiring careful management of fluid balance and ensuring adequate preload to maintain cardiac output. Feeding intolerance can occur due to venous congestion, and close monitoring is necessary to differentiate between normal spitting up and signs of heart failure or RV dysfunction. Late-onset RV dysfunction may occur several days after repair, requiring ongoing monitoring and potential interventions. Adequate recognition and management of these complications are essential for optimal patient outcomes.
Post-Operative Care and Discharge Planning
Post-operative care for Tetralogy of Fallot patients focuses on maintaining balanced fluid status, optimizing preload, and minimizing RV afterload. Careful adjustment of fluid levels is necessary to maintain cardiac output while avoiding pulmonary edema. Monitoring for arrhythmias, such as junctional ectopic tachycardia, is crucial for appropriate management. Successful extubation should be prioritized when feasible, aiming for early extubation to improve RV function and reduce afterload. Discharge planning involves consideration of potential long-term complications, such as RV dysfunction and pulmonary insufficiency. Follow-up care should be arranged to monitor for these complications and plan for future interventions, such as conduit placement or valve replacements if necessary.
Overview of Tetralogy of Fallot
Tetralogy of Fallot is a complex cardiac defect characterized by four specific abnormalities affecting the right ventricle, pulmonary artery, and aorta. These include pulmonary stenosis, ventricular septal defect (VSD), overriding aorta, and right ventricular hypertrophy. These defects are caused by an embryologic error in the conal septum development, resulting in malalignment and subsequent abnormalities. The severity of pulmonary stenosis determines the degree of cyanosis, with pink Tetralogy of Fallot exhibiting mild cyanosis and blue Tetralogy of Fallot being more severe. Surgical options for Tetralogy of Fallot range from complete repair in neonates with pink Tetralogy to palliative procedures in cyanotic infants. Post-operatively, monitoring for complications such as arrhythmias and RV dysfunction is crucial, and discharge planning should include follow-up care to address long-term complications and potential interventions.
Dr. Laura Ortmann is an Associate Professor in the Department of Pediatrics at the University of Nebraska College of Medicine. She serves as the Medical Director of the Cardiovascular Intensive Care Unit at Children’s Hospital and Medical Center in Omaha, Nebraska. She a CPR researcher and a great medical educator. She is a host on the Healing Hearts Podcast featuring her ongoing cardiac lesions series and produces MedEd videos on YouTube at DrOrtmannCICU.
After listening to this episode on Tetralogy of Fallot with Pulmonary Stenosis, learners should be able to:
Recognize the relevant preoperative anatomy that influences operative plan and postoperative care in the cardiac intensive care unit (CICU).
Recall the goals and general steps of operative repair.
Recognize the key information provided in surgical and anesthesia handover that will affect postoperative management.
Recognize the common and important postoperative complications and develop an approach to their management.
Develop a mental framework of the expected postoperative CICU course with a focus on common or important barriers to ICU discharge.
References:
Ortmann LA, Keshary M, Bisselou KS, Kutty S, Affolter JT. Association Between Postoperative Dexmedetomidine Use and Arrhythmias in Infants After Cardiac Surgery. World J Pediatr Congenit Heart Surg. 2019 Jul;10(4):440-445. doi: 10.1177/2150135119842873. PMID: 31307294.
How to support PedsCrit: Please complete our Listener Feedback Survey Please rate and review on Spotify and Apple Podcasts! Donations are appreciated @PedsCrit on Venmo , you can also support us by becoming a patron on Patreon. 100% of funds go to supporting the show.
Thank you for listening to this episode of PedsCrit. Please remember that all content during this episode is intended for educational and entertainment purposes only. It should not be used as medical advice. The views expressed during this episode by hosts and our guests are their own and do not reflect the official position of their institutions. If you have any comments, suggestions, or feedback-you can email us at pedscritpodcast@gmail.com. Check out http://www.pedscrit.comfor detailed show notes. And visit @critpeds on twitter and @pedscrit on instagram for real time show updates.
Get the Snipd podcast app
Unlock the knowledge in podcasts with the podcast player of the future.
AI-powered podcast player
Listen to all your favourite podcasts with AI-powered features
Discover highlights
Listen to the best highlights from the podcasts you love and dive into the full episode
Save any moment
Hear something you like? Tap your headphones to save it with AI-generated key takeaways
Share & Export
Send highlights to Twitter, WhatsApp or export them to Notion, Readwise & more
AI-powered podcast player
Listen to all your favourite podcasts with AI-powered features
Discover highlights
Listen to the best highlights from the podcasts you love and dive into the full episode