BackTable Vascular & Interventional Ep. 527 Managing Hereditary Hemorrhagic Telangiectasia and Pulmonary AVMs with Dr. Clifford Weiss
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Mar 21, 2025 Dr. Clifford Weiss, the Director of the Johns Hopkins Vascular Anomalies Center, shares his expertise on hereditary hemorrhagic telangiectasia (HHT) and pulmonary AVMs. He discusses the critical role of early diagnosis and multidisciplinary teams in effective patient care. The conversation highlights evolving guidelines for intervention, the intricacies of embolization techniques, and the importance of genetic testing. Dr. Weiss also sheds light on innovative treatments and ongoing challenges in managing HHT, showcasing the impact of specialized care on patient outcomes.
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HHT: A Multi-System Disease
- HHT is a complex, multi-system disease requiring a multidisciplinary care team.
- Interventional radiologists play a crucial role, especially in treating pulmonary AVMs.
Family Screening for HHT
- Screen all direct relatives of diagnosed HHT patients.
- Genetic testing is ideal, but clinical and imaging screenings are alternatives.
The Role of Echocardiograms in HHT
- Agitated saline echocardiograms detect right-to-left shunts, crucial for HHT diagnosis.
- This helps assess shunt severity and guides further imaging decisions.