Iron Overload Cardiomyopathy

Patients with erysmogenic right ventricular cardiomyopathy, or ARVC, usually present between the second and fourth decades of life. The disease can manifest with ventricular arrhizmia or sudden cardiac death in young adult. MRI is important in evaluating RV dilation, impaired function, and regional wall motion abnormalities. Leaked linear enhancement of the RV has been reported in approximately two-thirds of cases. Iron deposition in the myocardium causes a lower T2 star values.